Антитела Rabbit anti-human Trifunctional enzyme subunit beta, mitochondrial polyclonal Antibody;Biotin conjugated

Rabbit anti-human Trifunctional enzyme subunit beta, mitochondrial polyclonal Antibody;Biotin conjugated

Объем	100 мкг
Синонимы	Trifunctional enzyme subunit beta, mitochondrial (TP-beta) [Includes: 3-ketoacyl-CoA thiolase (EC 2.3.1.16) (Acetyl-CoA acyltransferase) (Beta-ketothiolase)], HADHB
Клональность	Polyclonal Antibody
Организм	Human
uniprot	P55084
Иммуноген	Recombinant Human Trifunctional enzyme subunit beta, mitochondrial protein (35-283AA)
Источник	Rabbit
Видовая специфичность	Human
Применение	ELISA
Примечание	Defects in HADHB are a cause of trifunctional protein deficiency (TFP deficiency) [MIM:609015]. The clinical manifestations are very variable and include hypoglycemia, cardiomyopathy and sudden death. Phenotypes with mainly hepatic and neuromyopathic involvement can also be distinguished. Biochemically, TFP deficiency is defined by the loss of all three enzyme activities of the TFP complex.
Клональность1	Polyclonal
Изотип	IgG
Коньюгат	Biotin
Буффер	Preservative: 0.03% Proclin 300<br />Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
Форма	Liquid
Хранение	Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Метод очистки	>95%, Protein G purified
Абревеатура	Trifunctional enzyme subunit beta, mitochondrial protein
Области исследований	Cancer, Metabolism, Signal transduction
Ссылка на страницу на сайте производителя	ссылка

Область использования: Поликлональные антитела Cusabio	Производство:	Cusabio
	Метод:
	Объем:	100 мкг
	Кат. номер:	CSB-PA03035D0Rb
Цена (с НДС 20%):	по запросу	В корзину
Наименование: Антитела Rabbit anti-human Trifunctional enzyme subunit beta, mitochondrial polyclonal Antibody;Biotin conjugated / Rabbit anti-human Trifunctional enzyme subunit beta, mitochondrial polyclonal Antibody;Biotin conjugated. Примечание: дополнительная информация (на английском языке).