Объем | 100 мкл |
Синонимы | Ceroid-lipofuscinosis neuronal protein 5, Protein CLN5, |
Клональность | Polyclonal Antibody |
Организм | Human |
uniprot | O75503 |
Иммуноген | Synthesized peptide derived from internal of human CLN5. |
Источник | Rabbit |
Видовая специфичность | Human |
Применение | ELISA, WB,WB:1:500-1:3000 |
Примечание | This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.<br/><br/>Savukoski M., Nat. Genet. 19:286-288(1998).<br/>Dunham A., Nature 428:522-528(2004).<br/> |
Клональность1 | Polyclonal |
Изотип | IgG |
Коньюгат | Non-conjugated |
Буффер | Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol. |
Форма | liquid |
Хранение | Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. |
Метод очистки | The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen. |
Области исследований | Neuroscience |
Ссылка на страницу на сайте производителя | ссылка |
Western blot analysis of extracts from LOVO cells, using CLN5 antibody.
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