Объем | 100 мкл |
Синонимы | ceroid-lipofuscinosis neuronal protein 6, |
Клональность | Polyclonal Antibody |
Организм | Human |
uniprot | Q9NWW5 |
Иммуноген | Synthesized peptide derived from internal of human CLN6. |
Источник | Rabbit |
Видовая специфичность | Human |
Применение | ELISA, WB, IHC,WB:1:500-1:3000, IHC:1:50-1:100 |
Примечание | This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.<br/><br/>Ota T., Nat. Genet. 36:40-45(2004).<br/>The MGC Project Team, Genome Res. 14:2121-2127(2004).<br/>Mole S.E., Exp. Cell Res. 298:399-406(2004).<br/> |
Клональность1 | Polyclonal |
Изотип | IgG |
Коньюгат | Non-conjugated |
Буффер | Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol. |
Форма | liquid |
Хранение | Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. |
Метод очистки | The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen. |
Области исследований | Neuroscience |
Ссылка на страницу на сайте производителя | ссылка |
Western blot analysis of extracts from HeLa cells, using CLN6 antibody.
|
Immunohistochemistry analysis of paraffin-embedded human cervix tissue using CLN6 antibody.
|
| |