anti- Alpha galactosidase A antibodyСпецификацияClonality | monoclonal | Host | Mouse | Specificity | Human | Tested Application | ELISA, WB, IHC, IF | Delivery Time | 2 to 4 working days | Clone ID | 7F1 | Isotype | IgG2a | Form | liquid | Purification | Protein A+G purification | Purity | ≥95% as determined by SDS-PAGE | Uniprot ID | P06280 | Calculated MW | 49 kDa | Ссылка на страницу на сайте производителя | ссылка | Инструкция | PDF | Storage | PBS with 0.02% sodium azide and 50% glycerol pH 7.3,-20℃ for 12 months(Avoid repeated freeze / thaw cycles.) | Background | GLA, also named as Melibiase, Agalsidase and Alpha-galactosidase A, belongs to the glycosyl hydrolase 27 family. It hydrolyzes terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resulting from the deficient activity of GLA. Enzyme replacement therapy(ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease, a lysosomal storage disease. | Immunogen | galactosidase, alpha | Synonyms | Alpha galactosidase A, galactosidase, alpha | Recommended dilution | WB: 1:500-1:2000; IHC: 1:20-1:200; IF: 1:20-1:200 | Immunohistochemistry of paraffin-embedded human kidney tissue slide using FNab00330(GLA Antibody) at dilution of 1:50
| HeLa cells were subjected to SDS PAGE followed by western blot with FNab00330(GLA antibody) at dilution of 1:1000
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Информация для заказаОбласть использования: | Производство: | Fine Biotech | Метод: | Антитела | Объем: | 100µg | Кат. номер: | FNab00330 | Цена (с НДС 20%): | по запросу | В корзину | Наименование: anti- Alpha galactosidase A antibody. Примечание: |
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